Paediatric Course Module 4 ADV720
 
Paediatric Course Module 4 ADV720
08/11 - 11/11/2016
08:45 - 17:30
London
England

Dietetic Management of Inherited Metabolic Disorders

Course Content: Lectures, workshops and case studies:-

  • Protein Metabolism e.g. PKU, Tyrosinaemia, MSUD, Homocystinuria
  • Organic acidaemias and urea cycle disorders
  • Disorders of carbohydrate metabolism e.g. galactosaemia, glycogen storage diseases
  • Fatty acid oxidation and disorders of ketogenesis
  • Lipid disorderd e.g. Lipoprotein lipase deficiency, abetalipoproteinanemia
  • Emergency regimens
  • Management of newborn infants
  • Education of children with IMD and their families
  • Feeding problems in children with metabolic disorders
  • Biochemical monitoring of diet